Essential Elements of Care for the
Child with Sickle Cell Disease

1. Prompt medical care due to: increased susceptibility to infection and the high probability of splenic sequestration crisis.
2. Administer prophylactic penicillin.
3. Pneumovax immunization at 2 and 5 years of age and a booster every 5 years thereafter.
4. An initial and then annual pediatric hematology evaluations.
5. Family testing and genetic counseling for the parents, a "couple at risk".
6. Availability of prenatal diagnosis for "couples at risk".
7. Ongoing pediatric medical follow-up to include both sick and well child care.
8. Knowledge of Sickle Cell Disease and other Hemoglobinopathies.